Skip to main content

Table 1 Clinical examination at the renal biopsy

From: Atypical histological abnormalities in an adult patient with nephronophthisis harboring NPHP1 deletion: a case report

Hematological

 

Reference values

Blood biochemistry

Reference values

Immunological test

Reference values

 WBC

5700

3300 ~ 8600

/μl

TP

7.0

6.6 ~ 8.1

g/dl

CH50

59

25.0 ~ 48.0

U/μl

 Hb

10.2

11.6 ~ 14.8

g/dl

Alb

4.2

4.1 ~ 5.1

g/dl

C3

99

86 ~ 160

mg/dl

 Plt

28.2

15.8 ~ 34.8

× 104/μl

BUN

19

8.0 ~ 20.0

mg/dl

C4

24

17 ~ 45

mg/dl

    

Cre

2.03

0.46 ~ 0.79

mg/dl

IgG

1216

870 ~ 1700

mg/dl

Urinalysis

   

eGFR

26

60~

mL/min/1.73m2

IgA

228

110 ~ 410

mg/dl

 pH

7.335

5.0 ~ 8.0

 

Cystatin C

2.05

0.56 ~ 0.87

mg/dl

IgM

152

33 ~ 190

mg/dl

 Specific gravity

1.004

  

Na

141

138 ~ 145

mM/l

ANA

<× 40

~ 40

 

 Protein

< 20

 

mg/dl

K

4.1

3.6 ~ 4.8

mM/l

anti SSA-Ab

1.9

~ 7

U/ml

 RBC

< 1

 

/HPF

Cl

107

101 ~ 108

mM/l

anti SSB-Ab

< 1.0

~ 7

U/ml

 WBC

< 1

 

/HPF

Ca

8.5

8.8 ~ 10.1

mg/dl

MPO-ANCA

< 1.0

~ 3.5

U/ml

 U-NAG

1.4

0.7 ~ 11.2

μg/l

CRP

< 0.1

0.00 ~ 0.14

mg/dl

PR3-ANCA

< 1.0

~ 3.5

U/ml

 U-β2MG

805

~ 230

μg/l

HbA1c

5.7

4.9 ~ 6.0

%

anti GMB-Ab

< 2.0

~ 3

U/ml